1.3k likes | 9.82k Views
HYPOSPADIAS. Dr.GOVINDRAJAN Department of Urology and Renal Transplantation SRMC & RI. NORMAL PENILE ANATOMY. 2 Corpora Cavernosa, Corpus Spongiosum Enclosed In A Fascial Sheath- T.Albuginea Bucks Fascia, Thick Fibrous Envelope Connective Tissue, Dartos Fascia. HYPOSPADIAS.
E N D
HYPOSPADIAS Dr.GOVINDRAJAN Department of Urology and Renal Transplantation SRMC & RI
NORMAL PENILE ANATOMY • 2 Corpora Cavernosa, Corpus Spongiosum Enclosed In A Fascial Sheath- T.Albuginea • Bucks Fascia, Thick Fibrous Envelope • Connective Tissue, Dartos Fascia
HYPOSPADIAS • Hypo- below, Spadon- orifice • Urethral meatus opens on ventral side of the penis, proximal to the tip of glans penis • Incidence ……..1/125 to 1/250
EMBRYOLOGY • Cloacal membrane, genital tubercle, labioscrotal swellings • Androgen stimulation…phallus elongation • 3 phases of urethral formation • Posterior urethra formation • Anterior urethra formation • Glandular segment formation • Prepuce formation
CLASSIFICATION • Smith …….. • Able ……..I , II, III degree • Browne ……..Coronal - distal penile, proximal penile, penoscrotal, scrotal penile • Basrat …….. (post chordee release)
CLASSIFICATION (LOCATION) • DISTAL • Glandular, Coronal, Distal penile • MIDPENILE • Midshaft • PROXIMAL • Proximal penile, Penoscrotal, Scrotal, Perineal
ASSOSIATION WITH OTHER DEFECTS • Renal agenesis, dysplasia, reflux • Prostatic utricle • Hernia : 9% • Cryptorchidism : 9% • Father : 9% • Siblings : 14%
PARTS OF HYPOSPADIAS • Meatus … usually non-stenotic • Stenosis more common in distal hypospadias • Megalomeatus intact prepuce
SKIN….. • Ventral defect & dorsal hood • Urethral delta • Hood of monk….Cobra eyes • Defects of spongiosum • Defects of cavernosa • Defective urethral plate
CURVATURE • Skin attachments • Bucks defect • Urethral plate • Cavernosa defects • Problems of unhealthy urethra
CHORDEE WITHOUT HYPOSPADIAS • Primary penile curvature • Types • Without defects (2/3) • With defects (1/3) • Penile torsion • Deviation to left • Concealed hypospadias
DEVINE HORTON CLASSIFICATION • TYPE I : • SPONGIOSUM DEFECT • TYPE II : • BUCKS & DARTOS DEFECT • TYPE III : • DARTOS & SKIN DEFECT
HYPOSPADIAS & INTERSEX • ? Form of androgen insufficiency • Mixed gonadal dysgenesis • Androgen insensitivity • Testosterone synthesis defects • 5 alpha reductase defects
FEATURES OF REPAIR • Artificial erection ( Gittes & McLaughlin) • Meatal correction • Neourethral formation • Orthoplasty • Skin cover…. Neourethral cover • Dorsal prepuce : Tunica Vaginalis • Time of repair : 6months - 12months
CORRECTION OF CHORDEE AFTER ORTHOPLASTY • Nesbitt plication • T.A.P • Dermal graft • T.Vaginalis graft • Corporal resection
HCG BEFORE SURGERY • Increase in penile length • Meatal advancement by 5-20mm • Decrease in hypospadias • Decrease in chordee • Increased vascularity • Increased corporal thickness both proximal & distal
TREATMENT OPTIONS • GLANDULAR & SUBCORONAL • MAGPI • GAP • MIP • DISTAL PENILE • MATHEIU • SNODGRASS • DEVINE HORTAN • MUSTARDEE
TREATMENT OPTIONS… • MIDPENILE • SNODGRASS • ONLAY ISLAND PREPUTIAL FLAP • KING • HODGSON II • PROXIMAL PENILE • TRANSVERSE PREPUTIAL FLAP • HODGSON I • HODGSON III
TREATMENT OPTIONS… • POSTERIOR URETHRA • TRANSVERSE PREPUTIAL FLAP • TWO STAGED • BUCCAL….TUBULAR….GLANS CHANNEL • BAYRS… • CECIL • SMITH
COMPLICATIONS • BLEEDING & HEMATOMA • MEATAL STENOSIS • URETHROCUTANEOUS INFECTION • URETHRAL DIVERTICULA • RECURRENT CURVATURE / STRICTURE • BREAK DOWN