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Types of Biliary Atresia

Types of Biliary Atresia. Biliary Atresia. is a condition in which the normal extrahepatic biliary system is disrupted progressive damage of extrahepatic and intrahepatic bile ducts secondary to inflammation may occur, leading to fibrosis, biliary cirrhosis, and eventual liver failure

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Types of Biliary Atresia

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  1. Types of BiliaryAtresia

  2. BiliaryAtresia • is a condition in which the normal extrahepatic biliary system is disrupted • progressive damage of extrahepatic and intrahepatic bile ducts secondary to inflammation may occur, leading to fibrosis, biliary cirrhosis, and eventual liver failure • affects approximately 1 in 10,000-15,000 births and occurs in 2 distinct forms: fetal-embryonic and postnatal.

  3. Forms of BA • The fetal-embryonic form/ Syndromic BA (10-35%) • appears in the first 2 weeks of life • In this form, the bile ducts are discontinuous at birth, and 10-20% of affected neonates have associated congenital defects, including situsinversus, polysplenia, malrotation, intestinal atresia, and cardiac anomalies, among others. • The post/perinatal form/ Non-syndromic BA (65-90%) • This form is typically found in neonates and infants aged 2-8 weeks • Progressive inflammation and obliteration of the extrahepatic bile ducts occur after birth • An isolated anomaly and infants may have a short jaundice-free interval

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  5. Classification of BA • The French classification is based on the anatomical pattern of the extrahepaticbiliary tract remnant.

  6. French Classification

  7. Classification of BA The Kasai Classification System • Most widely used • Divides cases of biliaryatresia according to their location and degree of pathology

  8. Kasai Classification

  9. Classification of BA

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