1 / 8

ECTOPIA LENTIS

ECTOPIA LENTIS. 1. Acquired. 2. Isolated familial ectopia lentis. 3. Associated with systemic syndromes. Marfan syndrome. Weill-Marchesani syndrome. Homocystinuria. 4. Treatment options. Acquired ectopia lentis. Trauma. Stretched zonules. Buphthalmos. Megalocorne a.

hilary-crawford
Download Presentation

ECTOPIA LENTIS

An Image/Link below is provided (as is) to download presentation Download Policy: Content on the Website is provided to you AS IS for your information and personal use and may not be sold / licensed / shared on other websites without getting consent from its author. Content is provided to you AS IS for your information and personal use only. Download presentation by click this link. While downloading, if for some reason you are not able to download a presentation, the publisher may have deleted the file from their server. During download, if you can't get a presentation, the file might be deleted by the publisher.

E N D

Presentation Transcript

  1. ECTOPIA LENTIS 1. Acquired 2. Isolated familial ectopia lentis 3. Associated with systemic syndromes • Marfan syndrome • Weill-Marchesani syndrome • Homocystinuria 4. Treatment options

  2. Acquired ectopia lentis Trauma Stretched zonules • Buphthalmos • Megalocornea Anterior uveal tumours Degenerate eye

  3. Isolated familial ectopia lentis Autosomal recessive Pupil may be normal Pupil may be displaced in opposite direction (ectopia lentis et pupillae)

  4. Autosomal dominant Systemic features of Marfan syndrome • Arachnodactyly • Limb-trunk disproportion • Aortic dilatation, dissection • and regurgitation • Pectus excavatum • High-arched palate • Mitral valve prolapse

  5. Ocular features of Marfan syndrome Lens Retinal detachment • Lattice degeneration • Axial myopia • Upward subluxation • Zonule usually intact Angle anomaly and glaucoma Cornea plana Blue sclera

  6. Autosomal recessive Weill-Marchesani syndrome Systemic features Ocular features • Microspherophakia • Short stature • Usually anterior lens subluxation • Short stubby fingers (brachydactyly) • Angle anomaly and glaucoma • Mental handicap

  7. Homocystinuria • Autosomal recessive • Defect in cystathio beta-synthase Systemic features Ocular features • Downward lens subluxation • Malar flush and fine, fair hair • Marfanoid habaitus • Disintegration of zonule • Increased platelet stickiness • Mental handicap

  8. Treatment Options for Ectopia Lentis 1. Spectacle correction • For induced astigmatism • For aphakic portion 2. Nd:YAG laser zonulysisto displace lens out of visual axis 3. Surgical removal • Associated cataract • Lens-induced glaucoma • Endothelial touch • When other methods are inappropriate

More Related