100

1. A.L.L. Encephal -opathies Neuro- Embrology SIDS ALTE Rickettsial Diseases 25 25 25 25 25 Teams J E O P A R D Y 50 50 50 50 50 Rules 75 75 75 75 75 . 100 100 100 100 100 Tie Breaker 150 150 150 150 150 Daily Double 200 200 200 200 200 Final

2. 25 pts • The inheritance pattern of hypermobility syndrome is: • A. Autosomal dominant • B. Autosomal recessive • C. X-linked • D. All of the above • Answer: D Return to main screen

3. 50 pts Marfan syndrome is characterized by all of the following EXCEPT A. Arachnodactyly B. Mitral valve prolapse C. Mental retardation D. Myopia answer: C Return to main screen

4. 75 pts Characteristics of Ehlers-Danlos syndrome include all of the following EXCEPT: A. Supravalvar aortic stenosis B. “Cigarette paper” scars C. Colon rupture D. Congenital hip dislocation Answer: A Return to main screen

5. 100 pts Which of the following is the MOST appropriate management of a child with hypermobility syndrome? A. Echocardiogram B. Slit lamp exam C. Urine amino acid analysis D. Reassurance Answer: D Return to main screen

6. 150 pts Which entity will most likely manifest respiratory dysfunction in infancy? A. Marfan syndrome B. Osteogenesis imperfecta C. Stickler syndrome D. Williams syndrome Answer: C Return to main screen

7. 200 pts Which of the following conditions is associated with dislocated lens? A. Ehlers-Danlos syndrome B. Homocystinuria C. Hypermobility syndrome D. Osteogenesis imperfecta answer: B Return to main screen

8. 25 pts Which of the following is MOST associated with a serum sickness-like reaction: A. Cefixime B. Cefaclor C. Cefuroxime D. Cephalexin Answer: B Return to main screen

9. 50 pts Ceftriaxone should not be administered to neonates because it may A. cause a rapid hemolytic anemia B. displace bilirubin from albumin C. cause a disulfuram-like reaction D. form immune complexes with maternal antibody Answer: B Return to main screen

10. 75 pts Which one of the following is an oral third generation cephalosporin? A. Loracarbef B. Cephradine C. Cefuroxime D. Cefetamet answer: D Return to main screen

11. 100 pts Which one of the following regarding cephalosporins is FALSE? A. Cephs are bactericidal B. Cephs bind penicillin-binding proteins C. Cephs are resistant to B-lactamases D. Cephs disrupt cell wall synthesis answer: C Return to main screen

12. 150 pts Production of cephalosporinases occurs commonly in all of the following EXCEPT A. Pseudomonas B. Citrobacter C. Enterobacter D. H influenza answer: D Return to main screen

13. 200 pts Which cephalosporin is most active against B fragilis? A. Ceftriaxone B. Cefoxitin C. Cefotaxime D. Cefazolin Answer: B Return to main screen

14. 25 pts The most common acute complication of acute nasal septal hematoma is: A. Cavernous sinus thrombosis B. Osteomyelitis C. Meningitis D. Nasal septal abscess Answer: D Return to main screen

15. 50 pts The classic brain tumor headache - progressive, worse in the morning, associated with nausea and vomiting - occurs in: A. Most patients with brain tumors B. A minority of patients with brain tumors C. No patients with brain tumors D. All patients with brain tumors answer: B Return to main screen

16. 75 pts Among the following, the finding MOST likely to be associated with aspiration of a hydrocarbon is: A. Bacterial tracheitis B. Diffuse atelectasis C. Esophageal stricture D. Pulmonary hemorrhage Answer: B Return to main screen

17. 100 pts The commonly isolated bacteria from nasal septal abscesses include all of the following EXCEPT: A. S aureus B. H influenza C. S pneumoniae D. Anaerobes Answer: D Return to main screen

18. 150 pts Which of the following best distinguish Crohn’s disease from ulcerative colitis? A. Crypt abscesses B. Mucosal ulcerations C. Hepatic involvement D. Noncaseating granulomas answer: D Return to main screen

19. 200 pts Which one of the following is the most common form of migraine headache? A. Migraine with aura B. Migraine without aura C. Complicated migraine D. Migraine multiplex answer: B Return to main screen

20. 25 pts Which of the following is false regarding G6PD? A. Most common metabolic disease of red cells B. Usually asymptomatic unless there is an oxidative stress C. Uncommon in African-Americans D. Common in Asains answer: C Return to main screen

21. 50 pts Characteristics of Wiskott-Aldrich Syndrome include all of the followng EXCEPT A. Recurrent infection B. Thrombocytopenia C. Elevated IgM D. Eczema answer: C Return to main screen

22. 75 pts Erythromycin does NOT do which of the following: A. Elevate theophylline levels B. Decrease digoxin levels C. Cause torsade when given with astemizole D. Enhance the anticoagulant effect of warfarin Answer: B Return to main screen

23. 100 pts X -linked Agammaglobulinemia is characterized by all of the following EXCEPT A. Lymphadenopathy B. Asymptomatic neonatal course C. Infection by encapsulated organisms D. Sinopulmonary infections answer: A Return to main screen

24. 150 pts Which of the following is NOT a characteristic of Ivemark syndrome A. Polysplenia B. Bilateral trilobed lungs C. Centrally located liver D. Complex congenital heart disease answer: A Return to main screen

25. 200 pts Repeated meningococcal and/or disseminated gonococcal infections are associated with: A. C 2 deficiency B. C 3 deficiency C. Combined C 2, 3, and 4 deficiency D. Combined C 5 through 9 deficiency answer: D Return to main screen

26. 25 pts Subacute bacterial endocarditis following a tooth extraction is most likely caused by A. Staph aureus B. H influenza (PREP) C. Strep viridans D. Staph epidermidis answer: C Return to main screen

27. 50 pts A newborn has bilateral aniridia. What condition should this child be screened for? A. Hearing loss (PREP) B. Agenesis of the corpus collosum C. RTA D. Wilm’s tumor answer: D Return to main screen

28. 75 pts Of the following skills, the one accomplished MOST consistently by a 4 yo child is: A. Understanding four prepositions B. Copying a triangle (PREP) C. Repeating five digits D. Answering nebulous developmental questions Answer: A Return to main screen

29. 100 pts A 15 month old is found to have ascariasis after a trip to the Caribbean. The BEST treatment would be A. Iodoquinol B. Metronidazole (PREP) C. Praziquantel D. Pyrantel pamoate Answer: D Return to main screen

30. 150 pts A 4 month old is mildly cyanotic but otherwise in no distress. The cyanosis is MOST likely caused by A. ASD B. PDA (PREP) C. Pulmonic stenosis D. TOF answer: D Return to main screen

31. 200 pts A personal or family history of which of the following is most likely to increase the risk for postpartum psychiatric illness? A. Anxiety disorder B. Bipolar disorder C. Dysthymia D. Schizophrenia answer: B Return to main screen

32. Peds in Review JeopardyTeams PL-1PL-2PL-3 Stevens Querry Murray Bauer Brown Theado Urban Kehrberg Beaves Return to main screen

33. NEW RULES If you are wrong, you LOSE points!! Some PREP questions have been added in. You have one minute to answer each question. Return to main screen

34. Return to main screen

35. TIE BREAKER Return to main screen

36. DAILY DOUBLEbet as much as you want!! In “Analgesia for Neonatal Circumcision: A Randomized Trial of EMLA vs. Dorsal Penile Nerve Block” by Butler-O’Hara; what is the conclusion? Answer: DPNB provides better pain reduction than EMLA. EMLA is superior to no anesthetic. Return to main screen

37. FINAL JEOPARDY Describe the clinical features of allergic bronchopulmonary aspergillosis. Episodic wheezing, expectoration of brown mucus plugs, low grade fever, eosinophilia, transient pulmonary infiltrates. Occurs most frequently in patients with chronic asthma or CF. Return to main screen