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Congenital Scoliosis: Treatment Options and Challenges. Mohammed Attiah, MB,Ch.B. FRCSC Assistant Professor,Orthopaedic Surgery UQU Orthopaedic Specialty Hospital Jeddah - Saudi Arabia. Review. Definition Spine Growth Facts Associated Anomalies Natural History. Challenges
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Congenital Scoliosis: Treatment Options and Challenges Mohammed Attiah, MB,Ch.B. FRCSC Assistant Professor,Orthopaedic Surgery UQU Orthopaedic Specialty Hospital Jeddah - Saudi Arabia
Review Definition Spine Growth Facts Associated Anomalies Natural History Challenges Decision making Treatment Options Controversies
Spinal Deformity with the Presence of Vertebral-Anomalies Congenital Scoliosis
Big Deal, Why? • Osseous Development • Neural Element • Sagittal Natural Curves • Symmetric Growth
Spine Growth Longitudinal Growth Chondro-epiphyseal portion of the end plate Endo-chondral Ossification Circumferential growth Posterior growth ( 5-8 y) Laminar growth Pedicular growth Anterior Growth(Pre-Pub yrs) Latitudinal Growth Perichondral & Periosteal apposition Taylor,J. Anat. (1975), 120, 1, pp. 49-68
Spine Growth Facts ? In utero = Extremely Accelerated Birth -2y = Increased Rate 2y - 10 y = Steady Rate Pre-pub = Increased Rate Thoracic Vertebra = 0.8 mm /y Lumbar Vertebra = 1.1 mm /y Thoracic Disc = 0.2-0.6 mm /y Lumbar Disc = 0.3-0.8 mm/y Hefti, JBJS Br, 1983;65:247-54 Dimeglio, Acta Orthop Belg,1990 Taylor, J Anat,1975
Thoracic Spine = 1.2 cm/ Year Lumbar Spine = 0.7 Cm / year Spine Growth Facts ? Dimeglio, Acta Orthop Belg,1990 Taylor, J Anat,1975
Associated Anomalies Pulmonary Compromise Rib Deformity Spinal Deformity Lung Congenital Abnormality Congenital Heart Disease 15 % Echo / Cardiology Consult CT chest measurement PFT volume depletion VC < 50% = Post Op Pulmonary complication Campbell, JBJS AM, 2004 Wezeka, Spine, 2004 Meehan, J Ped Ortho,1985 Reckles, JBJS, 1975 Ferguson, J Ped Orthop ,1996
Renal Anomalies 20-40 % Unilateral kidney Ureteric duplication Ureteric obstruction Associated Anomalies Renal U/S Hensinger, JBJS,1974 MacEwen, JBJS, 1972
Spinal Cord Anomalies 20% Tethered cord Diastemetomyelia Fibrous Dural Band Intradural Lipoma Syringomyelia ACM Associated Anomalies Spine MRI Spine CT scan McMaster, Spine,1998
Natural History Type of Vertebral Anomalies Growth Potential Site of Anomalies McMastar, Spine, 1998 Winter, Ortho Clin North Am,1998
Type of Vertebral Anomalies Uni Un-segmented Bar + Hemi-vertebra Natural History McMastar, Spine, 1998 Winter, Ortho Clin North Am,1998
Natural History Growth Potential First 2 years Adolescent Growth Spurt McMastar, Spine, 1998 Winter, Ortho Clin North Am,1998
Site of Anomalies Thoracic > Lumbar Natural History McMastar, Spine, 1998 Winter, Ortho Clin North Am,1998
Early stage of life Cause large deformity Rigid Curve Resistant to correction Progressive Associated anomalies Congenital Curves Challenges Prediction about what will happen with growth is very difficult McMaster, JBJS.1982 Fernandes, JBJS,2007
Decision Making Diagnosis Full Work Up Consultation Magnitude of Curve Age Type / Location of Anomaly Early Treatment Decision
Balanced Spine Stop progression Deformity Correction Growing Vertebra Growing Neural Element Torso - Leg ratio Treatment Goal What do you want? : What does the spine do?:
Low Risk for Progression Cobb angle < 25˚ RAVD < 20 ˚ High Risk for Progression Cobb Angle > 25˚ RAVD > 21˚ Initiation of Treatment Mehta, JBJS,Br, 1972
When to start Treatment Anticipated or actual curve progression Curve progression 10 ˚ Initial curve > 30 ˚ at growth spurt stages Mehta, JBJS,Br, 1972
Treatment Option Bracing Mixed anomalies Progressive secondary curve Controlling long,flexible compensatory curve below congenital anomalies Not Successful Treatment Option
Prevent Future Deformity In Situ Fusion Correct Present Deformity Gradual Correction Hemiepiphysiodesis Growing Nonfusion Rod Acute Correction Instrumentation & Fusion Hemivertebra Excision Osteotomy Surgical Treatment Options
In situ Fusion No hope to get congenitally fused side growing again Simplest & Safest solution Stop growth on convex side Unilateral Unsegmented Bar Balanced Not large curve < 40 ˚ Early stages of life McMaster, Spine, 1998 Dubousset, J Pedi Orthop,1998 Keller,lindesth, spine.1994
In situ Fusion Controversy Age Very early years of life? Anterior & Posterior fusion ? Combined Less potential anterior growth Abnormal anterior vessels Trans-pedicular approach Decorticating the spine Facet Fusion One level cephalad One level caudad McMaster, Spine, 1998 Dubousset, J Pedi Orthop,1998 Keller,lindesth, spine.1994
Prevent Future Deformity In Situ Fusion Correct Present Deformity Gradual Correction Hemiepiphysiodesis Growing Nonfusion Rod Acute Correction Instrumentation & Fusion Hemivertebra Excision Osteotomy Surgical Treatment Options
FAILURE OF FORMATION CONCAVE FUTURE GROWTH Single Hemi-vertebra Curve < 50 ˚ Age < 5 years Hemiepiphysiodesis & Hemiarthrodesis Keller,J Ped Orthop B,1994 Winter,J Ped Orthop,1981 Andrew, JBJS Br,1985
Failure to achieve correction High failure rate 30 % improvement ? 40 % no change 20 % progressed Average correction 10˚ Hemiepiphysiodesis Controversy Roaf, JBJS Br,1963 Keller, Spine,1994
Growing Non-Fusion Rod Very Young child Treat the extended Secondary Curve Akbarnia,McCarthy,SRS,1994
Growing Non-Fusion Rod Primary curve should be addressed: In Situ fusion Hemiepiphysiodesis Excision Osteotomy Not commonly used technique Lack of strong evidence & F/U
Hemivertebra Excision Popular procedure Immediate Excellent Bradford,JBJS Am,1990 Remove the Etiology Prevent worsening Correction
Hemivertebra Excision Ideal indication Hemivertebra LS junction Ignored large curve
Combined Vs Staged Anterior Approach Posterior Approach Leatherman,JBJS Am, 1996 Single Approach Posterior Excision Eggshell procedure Hemivertebra Excision
Complication Blood loss Segmental Epidural Neurological injury Cord injury Root injury Winter,spine, 1989 Wiles, JBJS Am,1951
Instrumentation & Fusion Safe correction Balanced spine Spinal cord status Fusion level selection 9 Yrs 8 yrs 40 80
Downside of Long Segment Fusion Crankshaft Phenomenon Less anterior growth rate No absolute grantee technique Sanders, JBJS Am,1995
Spine Osteotomy Short Segment Osteotomy
Spine Osteotomy Long Segment Osteotomy Unacceptable cosmetic Fixed deformity Unbalanced No other solution Salvage procedure Experienced spinal surgeon 40 40
Principles of Spine Osteotomy Cutting through anterior fusion mass Resection of enough bone to allow correction Temporarily stabilize curve Compressive instrumentation allow closure of osteotomy Bone graft ++++
Summary Challenges Decision making Treatment Options Safe Correct decision Long term Follow Up
Orthopaedic Specialty Hospital - OSH Jeddah - Saudi Arabia www.osh.med.sa