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Learn about paediatric hearing loss, common types, diagnosis methods, and treatment options by Dr. Nirmal Patel, Associate Professor of Surgery. Early detection is crucial for successful intervention.
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Paediatric Hearing Loss Dr Nirmal Patel MBBS (Hons)(Syd) FRACS (OHNS) MS (UNSW) Associate Professor of Surgery (Macquarie University) Director, Kolling Deafness Research Centre (University of Sydney)
Summary • Introduction • Conductive Hearing Loss • Sensorineural Hearing Loss • Diagnosis • Treatment
Introduction • Hearing loss is common • 1 in 1000 babies have significant hearing loss at birth • 10 in 1000 children have significant hearing loss at school (inc. mild and moderate) • 80% of all children will have at least one middle ear infection
And Mild Unilateral Hearing Loss has an Impact... • Significant reduction in language acquisition and speech with prolonged mild unilateral hearing loss. http://www.cdc.gov/ncbddd/ehdi/documents/unilateralhl/Mild_Uni_2005%20Workshop_Proceedings.pdf
Paediatric Conductive Loss • Congenital • Atresia of ear • Congenital stapes fixation • Cholesteatoma • Acquired • Acute and chronic otitis media
Paediatric Sensorineural Loss • Sensorineural Hearing Loss (Nerve deafness) • Genetic and Idiopathic (70%) • Acquired (30%) • Low birth weight/ NICU residents • Hyperbilirubinaemia • Ear and Head trauma • Anoxia and Hypoxia • Ototoxic Drugs and Chemicals • Infectious Diseases • Recurrent otitis media
Diagnosis • SWISH (Statewide Infant Hearing Screening Programme) aims to test every child born in NSW and identify significant hearing loss by the age of 3 months • Parental (other carers) clues • Family physician
Diagnosis • History • Risk factors for SNHL • Auditory milestones: • 3 months: Startled by loud sounds and calmed by familiar sounds • 6 months: ability to localise • 9 months: respond to name & mimic environmental sounds • 12 months: First meaningful words • 18 months: Vocabulary of 20 words or more • 24 months: Small sentences
Diagnosis • Examination • Local • Auricle • Canal • Tympanic membrane (pneumatic otoscopy) • Regional • Syndromic features • Tuning Forks • Difficult under 6 yrs
Diagnosis • Investigations • Hearing test - refer to audiologist with children’s experience
Diagnosis • Refer to ENT if concerned • Tests if suspecting SNHL • Imaging - CT, MRI (dysplasias, large vestibular aqueduct) • TFT (Pendred’s syndrome) • Urinalysis (Alport’s) • Liase with opthalmologist (Usher’s Syndrome), geneticist (Connexin 26) Hart CK, Choo DI Laryngoscope April 2013
Treatment for Conductive Hearing Loss - Chronic Otitis Media • Observation - minimise day care exposure and passive smoking, reflux disease (prevalence 48%) • Autoinflation/ otovent - low cost no adverse effects, reasonable to consider; cochrane review small studies no significant benefit. • Nasal Steroids, antihistamines,antibiotics - no evidence to support use. Largest effect when used for 4 weeks to 3 months. American Academy Otolaryngology, Pediatrics & Family Physicians Consensus 2005 Miura et al OHNS March 2012 Cochrane Review Oct 2010, Sept 2011 and Sept 2012
Treatment for Conductive Hearing Loss - Chronic Otitis Media • Middle Ear Ventilation Tubes (Grommets) - effect is small is normal speech and development. Likely significant effect in either speech/ hearing delayed child or developmental delayed child. Measures of disease specific quality of life improve in all studies. • Children <24 months untreated have a higher risk of speech and language delay. • Hearing Aids - poor compliance, fluctuating pathology therefore difficult to fit, damage. American Academy Otolaryngology, Pediatrics & Family Physicians Consensus 2005 Miura et al OHNS March 2012 Cochrane Review Oct 2010, Sept 2011 and Sept 2012
Treatment for Paediatric Sensorineural Hearing Loss • Hearing assistive techniques • Preferential seating • Techniques to use at home • Rehabilitation • Hearing Aids • FM systems • Cochlear Implantation
Summary • Hearing loss in children is common and significantly impacts speech and development even in mild unilateral loss. • Early diagnosis is the key to treatment success.
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