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Pediatric and Neuromuscular Orthopedics. Objectives. 11%-self-care-comfort -avoid complications Identify signs and symptoms in selected pediatric and neuromuscular disorders. Outline nursing interventions for medical and surgical protocols.
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Objectives • 11%-self-care-comfort -avoid complications • Identify signs and symptoms in selected pediatric and neuromuscular disorders. • Outline nursing interventions for medical and surgical protocols. • List strategies to maximize function in patients and families with neuromuscular disorders
Development • Infancy 0-18 months • Toddler 18 mos – 3 yrs • Pre-school 3-5 yrs • School age 6-12 yrs • Adolescence 13 –19
Pediatric Differences • Visualization • ossification • ultrasound • X-ray • Bone • Thick periosteum • Metaphyseal growth • Re-modeling
Nursing Intervention • Nursing see Table 11-1 from Core Curriculum 4th ed. • Child’s developmental level • Parent and child’s ability to learn • Amount disorder interferes with: • ADLs • Growth • Learning Ability • Social Adjustment
Nursing Intervention Parents • Realistic expectations • Understanding of the disease/disorder • Follow-up with treatment • Response to public inquiry
Nursing Intervention • Team approach • Include child in decisions • Play • Independence, socialization, • Creativity, problem solving
Upper Extremity Disorders • Congenital anomalies • Syndactyly webbing 2+ digits • Polydactyly extra digits • Congenital amputations /deficiencies • Brachial plexus injuries
Lower Extremity Disorders • DDH • Legg-Calvé-Perthes • Intoeing, torsional problems • SCFE (presentations) • Limb length inequality • Osteomyelitis, septic joint • Trauma
Developmental Dislocation of the Hip • DDH • F>M 1:500-1000 births • Breech, 1st born • Family history
Developmental Dislocation of the Hip • Physical Exam - hip clicks and clunks • Barlow’s – push hip out back • Ortolani’s abduct click in • Decreased abduct • Unequal skin folds • Ultrasound - X-ray
DDH Rx • Pavlik, abd. splint • Traction Bryant’s/ mod Bryant's • Surgical reduction closed vs open • Spica cast
DDH Nursing Care • Traction • Neurovascular Exam • Amputation 2° necrosis • Cast syndrome • Can be fatal
Talipes Equinovarus • “Clubbed Foot” 1.24:1000 births • M 2x > F • Inversion adduction and equinus of the forefoot • Fixed rigid deformity • Etiology: controversial • Uterine position • Idiopathic
Talipes Equinovarus • Dx: clinical apparent • Calf smaller, Achilles short • Rx:Stretching • Casting • Surgical releases
Talipes Equinovarus • Nursing, watch toes in cast • Foot will be smaller! • Rocker bottom from push up on metatarsals • Can play sports
Intoeing • Most common complaint! • Metatarsus adductus (foot deformity) • Tibial torsion • Femoral anteversion
Metatarsus Adductus • Foot deformity • 1:1000 births • Dx: exam • Rx: stretching • long leg molded cast • surgery
Tibial Torsion • Physiologic bowing of tibia • 2º intrauterine position • NORMAL for toddler • No treatment unless present at 8 years of age • Nursing - bring grandparent to appointment
Femoral Anteversion • Curvature of the femur • After 3 yrs resolves by 8yrs • Brace not effective • Osteotomy if functional problems after 8 yrs
Va us cubitus valgus cubitus varus coxa vara coxa valga genu valgum genu varum heel valgus hallux valgus heel varus metatarsus varus
Genu Valgus • Knock knees • Joint laxity -medial collateral ligs. • Common: 3 - 5 years • improves by 7 years • normal angulation • girls: 7 - 9° valgus • boys: 4 - 6° valgus
Genu Varus • ^ dist between knees >2.5 cm • W/ ankles together • external torsion of femur • improves spontaneously by 18 - 24 mos • in early amb & heavy children
Blount’s Disease • X-ray changes medial prox tibia • 50% unilat. tibial bowing • ^Black, ^obese, • Rx: no Δ 6 mos bracing • Surgical >30 mos old w/o Rx or structural / functional deform
Blount’s Disease • Rx: • Corrective prox. osteotomy. • Hemiepiphysiodesis • External fixator • Some with gradual correction
Osteogenesis Imperfecta “OI” • Brittle bone disease fracture with minimal stress • Multiple types some fatal • Etiology: autosomal dominant vs. recessive • Defect collagen synthesis • 1:20,000 births
Osteogenesis Imperfecta “OI” • Dx: Clinical deformities • Blue sclera, shepherds crook deformity • Dentinogenesis, deafness • Radiographs • Biopsy • Bone density
Osteogenesis Imperfecta “OI” • Rx brief Light wt. immob • I-M rods “Bailey” grows with child • Pamidronate treatment • Pain meds. • “Brittle baby” NO BP’s signs Don’t pull limbs, • Physical NOT mental handicap • Encourage independence
Legg Calvé Perthes • Aseptic necrosis femoral head • Idiopathic vs heredity • M 4x >F 1:2000 births • Age 3-12 years
Legg Calvé Perthes • Sx: Knee, hip, thigh pain • Limp • Decreased ROM • Dx: exam / X-ray
Slipped Capital Femoral Epiphysis Endocrine/ obesity/ growth / trauma • F 8-15yrs. M 10-17yrs • 1 : 10,000 adolescents • Sx: Hip, knee, pain (long duration) • Limp, decreased ROM • Dx: Hallmark sign- lack of internal rotation • X-ray -“Ice cream falling off the cone
Slipped Capital Femoral Epiphysis • Rx: bedrest, • N W B, crutches • Surgical pinning • Teach S&S for other hip - >50%
Limb Length Inequality • Congenital vs acquired • Sx: short limb, limp, back pain • Dx: X-ray, CT, bone age
Limb Length Inequality Rx: • < 2cm no treatment • 2-6 cm lifts epiphysiodesis • >6 - 15cm shorten opposite limb • Limb lengthening, external fixation
Limb Length Inequality • Nursing • Pain management • Pin care • Compartment syndrome • Emotional support
Osgood-Schlatter’s Disease • F 8-13 yrs M 11-15 yrs • Sx: painful swelling tibial tubercle • cosmetic deformity
Osgood-Schlatter’s Disease • Dx: exam • X-ray traction apophysitis • Rx: rest, ice, stretch hamstrings • Casting
Trauma • Leading cause of death in children • Common injuries (see table 11-3 ) • Child abuse – Battered Child Syndrome
Trauma: Child Abuse • 3.14 million children reported abused • Physical abuse • Greatest < 3 years (66-78%) • 30% under 6 mos
Salter-Harris Classification 1 2 4 5 3
Child Abuse - Fractures • Most common presentation! • >30% under 3 mos. • 70% under 6 mos.(1yr) are inflicted
Common Fractures Inflicted • Metaphyseal • Rib Fxs seen in 5-20% of abused • Scapular/distal clavicle/ night stick • Vertebral fx. or subluxation
Common Fractures Inflicted • Finger Fx. In non-ambulating child • Humerus Fx. (X supracondylar) < 3 Yrs. • Bilateral, multiple, or Fxs in different stages of healing • Complex skull Fx
Questions Linsey, 5 months old presents with knee swelling which of the following would prompt you to file for suspected child abuse: A. Septic joint with staph on aspiration B. Mongolian spots about the lower back C. Metaphyseal fractures of the distal femur D. Parent are obviously worried and seem really nice.
Questions Three year old Stephanie has a history on limping and refusing to put weight on her left leg. She is lying with her leg externally rotated. You are admitting her for: A. Traction to treat her Perthes disease and high fever. B. Observation for bracing of her septic hip. C. fever, high white count Perthes treatment. D. Severe malaise, fever, pre-op for septic hip aspiration.
Questions An 18 month old infant is admitted to your unit with a fractured femur. You notice blue sclera and shepherd crook deformities of his arms. You would: A. Hang “Brittle Baby” sign on his crib B. Change his diapers lifting him by the feet C. Keep his medication strictly by weight even if ineffective to prevent overdosing. D. Use real plasters for casting.
Achondroplasia • Most common dwarfing syndrome • 1 of every 26,000 live births M>F • Etiology: abnormal endochondral ossification • genetic defect autosomal dominant • 90% spontaneous mutations
Achondroplasia • Hypotonia resulting in slow motor development • C-spine injuries secondary to poor head control • Low back pain 2° to spinal stenosis • Thoracolumbar kyphosis hyperlordosis • longitudinal growth most affected • difficulty performing ADL’s
Scoliosis • Lateral curvature of the spine • Congenital • Paralytic • Neuromuscular • Idiopathic = most common