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1. Cleft Lip and Palate Dr. T. R. Stevenson
Division Head, Oral and Maxillofacial Surgery
Faculty of Medicine and Dentistry
University of Alberta
2. What is a Cleft? a fissure or elongated opening, especially one occurring in the embryo or derived from a failure of parts to fuse during embryonic
development
3. Variations of Cleft Lip and Palate
4. Embryology Palate forms between 5th and 6th week
Maxillary processes form maxilla and cheeks
Palatal processes form hard and soft palate
Lateral nasal processes form part of nose and
upper lip
Disruption in the fusion of any of the above processes can cause a cleft
5. Embryology
6. Incidence of Cleft Lip & Palate Most common oral-facial deformity
250,000 in North America
Over-all incidence 1:600- 750
Native American 1:300
African 1:2000
Caucasian 1:750
Asian 1:500
7. Distribution of Cleft Lip & Palate Cleft lip 21%
Cleft lip and palate 46%
Males > females (2:1)
Left > right > both (6:3:1)
Cleft palate 33%
females > males (2-4:1)
Submucous clefts 1:1200
8. Famous People with Clefts John Henry (Doc Holliday)
Tutankhamen
Tad Lincoln
Stacey Keach
9. Etiology of Cleft Lip & Palate Usually multifactorial: genetic and environmental
Isolated deformity: CL&P 85%, CP 58%
Disease of the mother
Parental age, viral infections, emotional stress, ETOH, smoking, poor nutrition, GH deficiency
Drugs
Dilantin, accutane, aminophylline, diazepam, anti-emetics, opiates, ASA
10. Etiology of Cleft Lip & Palate Social class
Lower socioeconomic level
Inadequate prenatal care
Genetic Factors
Multifactorial
Incidence varies among different racial groups
Twins are higher in monozygotic than dizygotic
Family history
Associated with other syndromes
11. When Cleft Lip and Palate Occurs Most serious congenital abnormality to affect oral-facial area
Can be catastrophic to parents and patient
Need for an informed explanation and reassurance
Initial appearance can be grotesque
Feeding and swallowing difficulty
Affects long term dental-facial growth
Psychological problems
Protracted therapy course, multiple operations to repair
Speech therapy
12. Cleft Lip and Palate Early repair can mean happy youth and healthy social life
In some countries not all patients have access to early repair
Isolation
Lack of education opportunities
Lack of work opportunities
Social outcasts
13. Psychosocial Issues: initial Must address from onset of care
Birth of a child alone is a time of family adjustment
Especially stressful with CL&P
Parents express sadness, guilt, anger and fear
Feeding difficulty, loss of ability to breast feed
Concern of accessing professional & community services
Financial concerns
Stress of surgery and the unknown
14. Psychosocial Issues: longer term Concerns about teasing, peer acceptance
Speech difficulties
Can become introverted
Increased risk of learning and behaviour problems
Children become part of decision process
Functioning in an appearance-conscious culture
Fear of future surgeries
High level of compliance needed for obturators, orthodontics, orthognathic surgery (burnout)
15. Cleft Team Members Plastic Surgeon
Pediatrician
Geneticist
Speech Therapist/ Pathologist
Oral and Maxillofacial Surgeon
Pediatric Dentist
General Dentist
Orthodontist
Social Worker
Psychologist
Audiologist
Parents
16. Treatment Sequence CL&P Neonatal (first four weeks)
First year
Second year
2nd to 6th year
6th to 12th year
12th to 18th year
17. Treatment Sequence CL&P Neonatal (first four weeks)
Pediatric and nursery care
Parental involvement, education and counselling
Treatment planning
Dental obturator if required
First Year
Preparation for surgery
Social and family planning
Primary lip repair
Dental, ENT and speech considerations
18. Treatment Sequence CL&P Second Year
Primary cleft palate repair
Speech and hearing evaluation
Management of ear infections, myringotomy tubes
Second to sixth year
Pharyngeal flap, if required
Dental evaluation and care
ENT evaluation and care
Educational assessment
General care
19. Treatment Sequence CL&P Sixth to twelfth year
Speech and hearing care
Dental, prosthetic and orthodontic care
Psychological, educational evaluation and intervention
Esthetic, secondary surgery if indicated
Alveolar cleft bone grafting
Twelfth to eighteenth year
Orthodontic and orthognathic therapy if indicated
Cosmetic counselling
Social counselling, vocational needs
Group therapy
Major restorative (prosthetics, implants etc.)
20. Treatment Outcomes
21. Treatment Outcomes
22. Surgical Phase
23. Surgical Phase
24. Operation Smile http://www.operationsmile.org