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Cord-blood transplants from unrelated donors in patients with Hurlers syndrome. Presented by:DR Ehab bader. Attended by:DR A. Hamam.
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Cord-blood transplants from unrelated donors in patients with Hurlers syndrome Presented by:DR Ehab bader. Attended by:DR A. Hamam
Hurlers syndrome is the most severe form of mucopolyasccharidosis,an AR metabolic storage disease caused by deficiency of alpha-L-iduronidase,result in accumulation of glycosaminoglycan in various tissues • Multi systemic affection. • BM transplantation can prevent the progression of enzyme deficiency and provides maximal benefit when performed early in life