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Proptosis From Neurofibroma (Kennerdell Case 66). John S. Kennerdell, MD Chair, Department of Ophthalmology Allegheny General Hospital Professor, Ophthalmology Drexel University College of Medicine.
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Proptosis From Neurofibroma (Kennerdell Case 66) John S. Kennerdell, MD Chair, Department of Ophthalmology Allegheny General Hospital Professor, Ophthalmology Drexel University College of Medicine
A 38-year-old man who was referred with chronic proptosis of the right eye with minimal visual disturbance. The proptosis measurements were 22 right and 18 left with a base of 106. There was no pain associated with the proptosis. Case 66 - Slide 1/14
A café au lait spot on the patient’s skin indicating a patient with neurofibromatosis. Case 66 - Slide 2/14
An axial CT scan of the irregular lesion in the superior right orbit with a variable internal consistency. Case 66 -Slide 3/14
The lower axial view of the lesion in the region of the right optic nerve. Case 66 -Slide 4/14
An unenhanced axial view of an MRI scan showing the lesion in the superior portion of the right orbit. Case 66 -Slide 5/14
An unenhanced coronal MRI showing the lesion in the superior right orbit as a rounded lesion in the region of the superior rectus muscle. Case 66 -Slide 6/14
The bony burr holes in the calvarium in the right frontal cranial orbitotomy being performed by a neurosurgeon. Case 66 -Slide 7/14
The removal of the calvarium to gain access to the lesion in the superior right orbit. Case 66 -Slide 8/14
The microscopic view of the reddish lesion in the superior right orbit. Case 66 -Slide 9/14
A cryoprobe extracting the rounded irregular lesion from the superior right orbit. Case 66 -Slide 10/14
The gross specimen of the solitary neurofibroma removed from the superior portion of the right orbit through the craniotomy. Case 66 -Slide 11/14
The bony craniotomy site being replaced Case 66 -Slide 12/14
The patient one month post-operatively with elimination of the right proptosis. He had no functional deficit. Case 66 -Slide 13/14
An overhead view of the patient’s eyes showing the symmetry of the forward placement of both eyes. Case 66 -Slide 14/14