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Congenital Urogenital Malformations. Prefinal. Topics . Renal agenesis Renal hypoplasia Renal fusion Ectopic kidney Ureteral atresia Duplication of the ureter Supernumerary kidneys. Renal agenesis. Virtually always unilateral. Kidney is either absent or undeveloped.
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Congenital Urogenital Malformations Prefinal
Topics • Renal agenesis • Renal hypoplasia • Renal fusion • Ectopic kidney • Ureteral atresia • Duplication of the ureter • Supernumerary kidneys
Renal agenesis • Virtually always unilateral. • Kidney is either absent or undeveloped. • Usually causes no symptoms and found incidentally.
Renal hypoplasia • May appear as one small kidney with the other one larger than normal. • Small kidneys also have small arteries and are associated with hypertension requiring nephrectomy.
Renal fusion (horseshoe kidney) • Prevalence 1 in 1,000 people. • Most frequent abnormality seen is a horseshoe kidney containing 2 excretory systems and 2 ureters. • Usually asymptomatic but are prone to obstruction.
Ectopic (Pelvis Kidney) • In simple ectopy, the kidney does not ascend properly and is found in the pelvis or over the brim. • Prone to obstruction and infection. • Less commonly crossed ectopy without fusion. The kidney then lies on the opposite side and is not attached to the normally placed kidney.
Ureteral atresia • The ureter may be absent or fails to extend to the bladder and therefore with a blind ending. • It is associated with ipsilateral absent or multicystic kidney. • Bilateral atresia is incompatible with life. Unilateral atresia is usually asymptomatic but may cause hypertension.
Duplication of the ureter • One of the most common congenital malformations of the urinary tract with duplication found in 0.9% of a series of autopsies. • More common in females and is often bilateral. • Often asymptomatic but commonly presents with persistent or recurrent urinary tract infections.
Supernumerary kidneys • Third kidney is very rare and not to be confused with the relatively common unilateral duplication of the renal pelvis.